Polysplenia Syndrome

Polysplenia syndrome is a congenital disorder that is a type of situs ambiguous characterized by left isomerism (bilateral left sidedness). In addition to multiple spleens, there are often cardiac anomalies, interruption of the IVC with azygos continuation, bilateral hyparterial bronchi, and abdominal heterotaxia.120,121 Most patients die by the age of 5 years because of the severe cardiac anomalies. However, the syndrome may be first seen in adulthood, particularly when there is no accompanying congenital heart defect120-122 (Figs. 2-63 and 2-64).

Essentials of Human Physiology

Essentials of Human Physiology

This ebook provides an introductory explanation of the workings of the human body, with an effort to draw connections between the body systems and explain their interdependencies. A framework for the book is homeostasis and how the body maintains balance within each system. This is intended as a first introduction to physiology for a college-level course.

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